THE "NEW FRONTIERS" OF ARRHYTHMIAS 1998

RT-244	Further observations of the Brugada-Martini syndrome. Familial distribution of the incomplete bundle branch block, STT. Elevation and sudden death syndrome. A clinical-morphologic and genetic study of nine families


Franco Naccarella, Angelo Rolli, Angelo Carboni, Angelo Finardi, Antonello Zoni, Giovannina Lepera, Gaetano Barbato, Massimo Palmieri, Pietro Ticci, Luigi Padeletti, Andrea NavaА, Bortolo MartiniА, Alessandra RampazzoАА, Gianantonio DanieliАА, Paola Bertaccini^, Rossella Fattori^, Giampaolo Gavelli^. Dipartimento di Cardiologia, Azienda Ospedaliera di Parma, Dipartimento di Cardiologia, Ospedale Maggiore, Bologna, АCattedra di Cardiologia, Universita di Padova, ААDipartimento di Genetica Medica, Universita di Padova, ^Dipartimento di Radiologia Medica III e NMR, Universita di Bologna, *Dipartimento di Medicina Interna e Cardiologia, Universita di Firenze, Italy

References
1.	Brugada P, Brugada J: A distinct clinical and electrocardiographic syndrome: right bundle branch block, persistent ST segment elevation with normal QT interval and sudden cardiac death (abstract). PACE 1991; 14: 746.
2.	Brugada P, Brugada J: Right bundle branch block, persistent ST segment elevation and sudden cardiac death: a distinct clinical and electrocardiographic syndrome. J Am Coll Cardiol 1992; 20: 1391-1396.
3.	Sicouri S, Antzelevitch C: A subpopulation of cells with unique electrophysiological properties in the deep subepicardium of the canine ventricle: the M cells. Circ Res 1991; 68: 1729-1741.
4.	Krishnan SC, Antzelevitch C: Flecainide-induced arrhythmia in canine ventricular epicardium. Phase 2 reentry? Circulation 1993; 87: 562-572.
5.	Brugada P, Wellens HJJ: Early afterdepolarizations: role in conduction block, "prolonged repolarization-dependent reexcitation", and tachyarrhythmias in the human heart. PACE 1985; 8: 889-896.
6.	Bjerregaard P, Gussak I, Kotar SL, et al: Recurrent syncope in a patient with prominent J wave. Am Heart J 1994; 127: 1426-1430.
7.	Tomaszewski W: Changements electrocardiographiques observes chez un homme mort de froid. Arch Mal Coeur 1938; 31: 525-528.
8.	Solomon A, Barish RA, Browne B, et al: The electrocardiographic features of hypothermia. Am J Med 1989; 7: 169-173.
9.	Emslie-Smith D, Sladden Ge, Stirling GR: The significance of changes in the electrocardiogram in hypothermia. Br Heart J 1959; 21: 343-351.
10.	Yan GX, Antzelevitch C: Cellular basis for the electrocardiographic J wave. Circulation 1996; 93: 372-379.
11.	Miyazaki T, Mitamura H, Miyoshi S, Soejima K, Aizawa Y, Ogawa S: Autonomic and antiarrhythimc drug modulation of ST segment elevation in patient with Brugada syndrome. J Am Coll Cardiol 1996; 27: 1061-1070.
12.	Proclemer A, Facchin D, Feruglio GA, Nucifora R: Fibrillazione ventricolare recidivante, blocco di branca destra, persistente sopraslivellamento del tratto ST in V1-V3; una nuova sindrome aritmica? G Ital Cardiol 1993; 23: 1211-1218.
13.	Atarashi H, Ogawa S, Harumi K, et al: Characteristics of patients with right bundle branch block and ST segment elevation in right precordial leads. Am J Cardiol 1996; 78: 581-583.
14.	Wever EFD, Hauer RNW, Oomen A, Peters RHJ, Bakker PFA, Robles de Medina EO: Unfavourable outcome in patients with primary electrical disease who survived an episode of ventricular fibrillation. Circulation 1993; 88: 1021-1029.
15.	Brugada J, Brugada P: Further characterisation of the syndrome of right bundle branch block, ST segment elevation, and sudden cardiac death. J Cardiovasc Electrophysiol 1997; 8: 325-331.
16.	Corrado D, Nava A, Buja G, et al: Familial cardiomyopathy underlies syndrome of right bundle branch block, ST segment elevation and sudden cardiac death. J Am Coll Cardiol 1996; 27: 443-448.
17.	Scheinmann MM: Is the Brugada syndrome a distinct clinical entity? J Cardiovasc Electrophysiol 1997; 8: 332-334.
18.	Rampazzo A, Nava A, Danieli GA, et al: The gene for arrhythmogenic right ventricular cardiomyopathy maps to chromosome 14q23. Hum Mol Genet 1994; 3: 959-962.
19.	Naccarella F, Barbato G, Palmieri M, Lepera G, Bracchetti D: Familial distribution of the incomplete bundle branch block, ST elevation and sudden death syndrome. A clinical-morphologic and genetic study of nine families (abstract). NASPE Meeting, New Orleans, 1997.

13th International Congress THE "NEW FRONTIERS" OF ARRHYTHMIAS 1998

January 24-31, 1998 Marilleva, Trento, Italy

RT-244

Further observations of the Brugada-Martini syndrome. Familial distribution of the incomplete bundle branch block, STT. Elevation and sudden death syndrome. A clinical-morphologic and genetic study of nine families

References

1.

Brugada P, Brugada J: A distinct clinical and electrocardiographic syndrome: right bundle branch block, persistent ST segment elevation with normal QT interval and sudden cardiac death (abstract). PACE 1991; 14: 746.

2.

Brugada P, Brugada J: Right bundle branch block, persistent ST segment elevation and sudden cardiac death: a distinct clinical and electrocardiographic syndrome. J Am Coll Cardiol 1992; 20: 1391-1396.

3.

Sicouri S, Antzelevitch C: A subpopulation of cells with unique electrophysiological properties in the deep subepicardium of the canine ventricle: the M cells. Circ Res 1991; 68: 1729-1741.

4.

Krishnan SC, Antzelevitch C: Flecainide-induced arrhythmia in canine ventricular epicardium. Phase 2 reentry? Circulation 1993; 87: 562-572.

5.

Brugada P, Wellens HJJ: Early afterdepolarizations: role in conduction block, "prolonged repolarization-dependent reexcitation", and tachyarrhythmias in the human heart. PACE 1985; 8: 889-896.

6.

Bjerregaard P, Gussak I, Kotar SL, et al: Recurrent syncope in a patient with prominent J wave. Am Heart J 1994; 127: 1426-1430.

7.

Tomaszewski W: Changements electrocardiographiques observes chez un homme mort de froid. Arch Mal Coeur 1938; 31: 525-528.

8.

Solomon A, Barish RA, Browne B, et al: The electrocardiographic features of hypothermia. Am J Med 1989; 7: 169-173.

9.

Emslie-Smith D, Sladden Ge, Stirling GR: The significance of changes in the electrocardiogram in hypothermia. Br Heart J 1959; 21: 343-351.

10.

Yan GX, Antzelevitch C: Cellular basis for the electrocardiographic J wave. Circulation 1996; 93: 372-379.

11.

Miyazaki T, Mitamura H, Miyoshi S, Soejima K, Aizawa Y, Ogawa S: Autonomic and antiarrhythimc drug modulation of ST segment elevation in patient with Brugada syndrome. J Am Coll Cardiol 1996; 27: 1061-1070.

12.

Proclemer A, Facchin D, Feruglio GA, Nucifora R: Fibrillazione ventricolare recidivante, blocco di branca destra, persistente sopraslivellamento del tratto ST in V1-V3; una nuova sindrome aritmica? G Ital Cardiol 1993; 23: 1211-1218.

13.

Atarashi H, Ogawa S, Harumi K, et al: Characteristics of patients with right bundle branch block and ST segment elevation in right precordial leads. Am J Cardiol 1996; 78: 581-583.

14.

Wever EFD, Hauer RNW, Oomen A, Peters RHJ, Bakker PFA, Robles de Medina EO: Unfavourable outcome in patients with primary electrical disease who survived an episode of ventricular fibrillation. Circulation 1993; 88: 1021-1029.

15.

Brugada J, Brugada P: Further characterisation of the syndrome of right bundle branch block, ST segment elevation, and sudden cardiac death. J Cardiovasc Electrophysiol 1997; 8: 325-331.

16.

Corrado D, Nava A, Buja G, et al: Familial cardiomyopathy underlies syndrome of right bundle branch block, ST segment elevation and sudden cardiac death. J Am Coll Cardiol 1996; 27: 443-448.

17.

Scheinmann MM: Is the Brugada syndrome a distinct clinical entity? J Cardiovasc Electrophysiol 1997; 8: 332-334.

18.

Rampazzo A, Nava A, Danieli GA, et al: The gene for arrhythmogenic right ventricular cardiomyopathy maps to chromosome 14q23. Hum Mol Genet 1994; 3: 959-962.

19.

Naccarella F, Barbato G, Palmieri M, Lepera G, Bracchetti D: Familial distribution of the incomplete bundle branch block, ST elevation and sudden death syndrome. A clinical-morphologic and genetic study of nine families (abstract). NASPE Meeting, New Orleans, 1997.

CARDIOnetЎ - registered trade mark name Copyright Љ 1996-1998 by CARDIOnet. All rights reserved.

13th International Congress
THE "NEW FRONTIERS"
OF ARRHYTHMIAS 1998

January 24-31, 1998
Marilleva, Trento, Italy

Brugada P, Brugada J:
A distinct clinical and electrocardiographic syndrome: right bundle branch block, persistent ST segment elevation with normal QT interval and sudden cardiac death (abstract).
PACE 1991; 14: 746.

Brugada P, Brugada J:
Right bundle branch block, persistent ST segment elevation and sudden cardiac death: a distinct clinical and electrocardiographic syndrome.
J Am Coll Cardiol 1992; 20: 1391-1396.

Sicouri S, Antzelevitch C:
A subpopulation of cells with unique electrophysiological properties in the deep subepicardium of the canine ventricle: the M cells.
Circ Res 1991; 68: 1729-1741.

Krishnan SC, Antzelevitch C:
Flecainide-induced arrhythmia in canine ventricular epicardium. Phase 2 reentry?
Circulation 1993; 87: 562-572.

Brugada P, Wellens HJJ:
Early afterdepolarizations: role in conduction block, "prolonged repolarization-dependent reexcitation", and tachyarrhythmias in the human heart.
PACE 1985; 8: 889-896.

Bjerregaard P, Gussak I, Kotar SL, et al:
Recurrent syncope in a patient with prominent J wave.
Am Heart J 1994; 127: 1426-1430.

Tomaszewski W:
Changements electrocardiographiques observes chez un homme mort de froid.
Arch Mal Coeur 1938; 31: 525-528.

Solomon A, Barish RA, Browne B, et al:
The electrocardiographic features of hypothermia.
Am J Med 1989; 7: 169-173.

Emslie-Smith D, Sladden Ge, Stirling GR:
The significance of changes in the electrocardiogram in hypothermia.
Br Heart J 1959; 21: 343-351.

Yan GX, Antzelevitch C:
Cellular basis for the electrocardiographic J wave.
Circulation 1996; 93: 372-379.

Miyazaki T, Mitamura H, Miyoshi S, Soejima K, Aizawa Y, Ogawa S:
Autonomic and antiarrhythimc drug modulation of ST segment elevation in patient with Brugada syndrome.
J Am Coll Cardiol 1996; 27: 1061-1070.

Proclemer A, Facchin D, Feruglio GA, Nucifora R:
Fibrillazione ventricolare recidivante, blocco di branca destra, persistente sopraslivellamento del tratto ST in V1-V3; una nuova sindrome aritmica?
G Ital Cardiol 1993; 23: 1211-1218.

Atarashi H, Ogawa S, Harumi K, et al:
Characteristics of patients with right bundle branch block and ST segment elevation in right precordial leads.
Am J Cardiol 1996; 78: 581-583.

Wever EFD, Hauer RNW, Oomen A, Peters RHJ, Bakker PFA, Robles de Medina EO:
Unfavourable outcome in patients with primary electrical disease who survived an episode of ventricular fibrillation.
Circulation 1993; 88: 1021-1029.

Brugada J, Brugada P:
Further characterisation of the syndrome of right bundle branch block, ST segment elevation, and sudden cardiac death.
J Cardiovasc Electrophysiol 1997; 8: 325-331.

Corrado D, Nava A, Buja G, et al:
Familial cardiomyopathy underlies syndrome of right bundle branch block, ST segment elevation and sudden cardiac death.
J Am Coll Cardiol 1996; 27: 443-448.

Scheinmann MM:
Is the Brugada syndrome a distinct clinical entity?
J Cardiovasc Electrophysiol 1997; 8: 332-334.

Rampazzo A, Nava A, Danieli GA, et al:
The gene for arrhythmogenic right ventricular cardiomyopathy maps to chromosome 14q23.
Hum Mol Genet 1994; 3: 959-962.

Naccarella F, Barbato G, Palmieri M, Lepera G, Bracchetti D:
Familial distribution of the incomplete bundle branch block, ST elevation and sudden death syndrome. A clinical-morphologic and genetic study of nine families (abstract).
NASPE Meeting, New Orleans, 1997.

CARDIOnet^Ў - registered trade mark name
Copyright Љ 1996-1998 by CARDIOnet. All rights reserved.